Fragile X Syndrome: Medical Considerations and Stomatological Aspects for Dental Treatment

Authors

  • Cristhiane Olívia Ferreira Do Amaral University of Oeste Paulista, Presidente Prudente, State of São Paulo, Brazil
  • Nilzete Santana Silva University of Western Sao Paulo, Presidente Prudente, State of São Paulo, Brazil
  • Alexsander Guedes University of Western Sao Paulo, Presidente Prudente, State of São Paulo, Brazil
  • Mariana Olívia Ferreira Do Amaral University of West São Paulo, Presidente Prudente, Sao Paulo, Brazil
  • Eliane Cristina Gava Pizi University of Western Sao Paulo, Presidente Prudente, Sao Paulo, Brazil
  • Fabiana Gouveia Straioto University of Western Sao Paulo, Presidente Prudente, Sao Paulo, Brazil

DOI:

https://doi.org/10.24203/ajas.v10i4.7020

Keywords:

Síndrome do X Frágil, Saúde Bucal, Condição Sistêmica, Transtornos Comportamentais ×

Abstract

The objective of this study was to carry out a literature review  in order to  elucidate general and oral physical aspects, behavioral disorders, medical considerations  and discuss   considerations  about the dental approach in individuals with Fragile X Syndrome (FXS) as well as to provide  surgeons dentists with   greater care clarification towards these patients. A literature review has been  carried out in the following databases: Virtual Health Library (VHL) –MEDLINE– PubMed , SciELO and in the  Capes database  Journals. The descriptors used were: Fragile X Syndrome, Oral Health, Systemic Condition, Behavioral Disorders. The main phenotypic characteristics found in the literature were: prominent ears, elongated face, strabismus, hyperextensible joints , macrorchidism , mitral valve prolapse, seizures. Fragile X Syndrome  oral characteristics  are: mandibular prognathism, atresic and deep palate, enamel hypoplasia, malocclusion, presence of biofilm due to unestablished hygiene habits, caries, calculus and gingivitis. Cognitive deficit, autism spectrum disorder, anxiety disorder and hyperactivity are behaviors found in FXS  which bring   difficulties for these patients to undergo  a dental approach. The dental surgeon must be up-to-date and aware of the medical and behavioral conditions of FXS individuals and, thus, offer an adequate and safe dental approach. Systemic, behavioral and oral abnormalities require an initial  dental treatment planning.

 

Author Biographies

  • Nilzete Santana Silva, University of Western Sao Paulo, Presidente Prudente, State of São Paulo, Brazil

    DDS - University of Western Sao Paulo - Unoeste, in the city of Presidente Prudente, State of São Paulo, Brazil: Dentistry participant in the Special Program for Scientific Initiation (PEIC/SPSI)

  • Alexsander Guedes, University of Western Sao Paulo, Presidente Prudente, State of São Paulo, Brazil

    DDS - University of Western Sao Paulo - Unoeste, in the city of Presidente Prudente, State of São Paulo, Brazil: Dentistry participant in the Special Program for Scientific Initiation (PEIC/SPSI)

  • Mariana Olívia Ferreira Do Amaral, University of West São Paulo, Presidente Prudente, Sao Paulo, Brazil

    Graduate student, Medical School, University of West São Paulo, Presidente Prudente, Sao Paulo, Brazil.

  • Eliane Cristina Gava Pizi, University of Western Sao Paulo, Presidente Prudente, Sao Paulo, Brazil

    DDS, Ms, PhD. Department of Dentistics, Dental School, University of Western Sao Paulo, Presidente Prudente, Sao Paulo, Brazil

  • Fabiana Gouveia Straioto, University of Western Sao Paulo, Presidente Prudente, Sao Paulo, Brazil

    DDS, Ms, PhD. Department of Prosthodontics and Geriatic Dentistry, Dental School, University of Western Sao Paulo, Presidente Prudente, Sao Paulo, Brazil

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Published

2022-09-10

Issue

Vol. 10 No. 4 (2022): August 2022

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Articles

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Copyright (c) 2022 Cristhiane Olívia Ferreira Do Amaral, Nilzete Santana Silva, Alexsander Guedes, Mariana Olívia Ferreira Do Amaral, Eliane Cristina Gava Pizi, Fabiana Gouveia Straioto

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How to Cite

Fragile X Syndrome: Medical Considerations and Stomatological Aspects for Dental Treatment. (2022). Asian Journal of Applied Sciences, 10(4). https://doi.org/10.24203/ajas.v10i4.7020